Immunoglobulin
Blood products
============
IVIG
Replacement therapy
Established
Immunomodulation
Established
NO ROLE
Acute optic neuritis
Acute rheumatic fever
Adrenoleukodystrophy
Amegakaryocytic thrombocytopenia
Antiphospholipid syndrome (non-obstetric)
Aplastic anaemia/pancytopenia
Asthma
Atopic dermatitis/eczema — adult
Autism
Autologous haemopoietic stem cell transplantation
Behçet’s disease
Cardiac surgery with bypass — prophylaxis
Congestive cardiac failure
Crohn’s disease
Diamond Blackfan syndrome
Female infertility
Glomerulonephritis — IgA nephritis
Haemolytic uraemic syndrome
Henoch–Schonlein purpura
HIV/AIDS — adult
Idiopathic dilated cardiomyopathy
Linear IgA disease
Lupus cerebritis
Lupus nephritis
Motor neuron disease/amyotrophic lateral sclerosis
Myalgic encephalomyelitis
Narcolepsy/cataplexy
Nephrotic syndrome
Obsessive compulsive disorders
Polyneuropathy of critical illness
Recurrent foetal loss (with or without antiphospholipid syndrome)
Rheumatoid arthritis
Sepsis
Sickle cell disease
Systemic lupus erythematosus (SLE)
Ulcerative colitis
============
IVIG
Replacement therapy
Established
- Acquired hypogammaglobulinaemia secondary to haematological malignancies
- Primary immunodeficiency diseases with antibody deficiency
- Secondary hypogammaglobulinaemia (including iatrogenic immunodeficiency)
- Specific antibody deficiency
- Acute leukaemia in children
- HIV in children
Immunomodulation
Established
- Chronic inflammatory demyelinating polyneuropathy
- Guillain–Barré syndrome
- Idiopathic (autoimmune) thrombocytopenic purpura (ITP) in adults
- Inflammatory myopathies (polymyositis, dermatomyositis, inclusion body myositis)
- Kawasaki disease
- Lambert–Eaton myasthenic syndrome
- Multifocal motor neuropathy
- Myasthenia gravis
- Neonatal haemochromatosis
- Stiff person syndrome
- Acute disseminated encephalomyelitis
- ANCA-positive systemic necrotising vasculitis
- Autoimmune haemolytic anaemia
- Bullous pemphigoid
- Cicatricial pemphigoid
- Evans syndrome - autoimmune haemolytic anaemia with immune thrombocytopenia
- Foeto-maternal/neonatal alloimmune thrombocytopenia (FMAIT/NAIT)
- Haemophagocytic syndrome
- Idiopathic (autoimmune) thrombocytopenia purpura (ITP) in children
- IgM paraproteinaemic neuropathy
- Kidney transplantation
- Multiple sclerosis
- Opsoclonus-myoclonus ataxia
- Pemphigus foliaceus
- Pemphigus vulgaris
- Post-transfusion purpura
- Toxic epidermal necrolysis/Stevens–Johnson syndrome (TEN/SJS)
- Toxic shock syndrome
- Autoimmune congenital heart block (neonatal lupus)
- Autoimmune neutropenia
- Autoimmune uveitis
- Catastrophic antiphospholipid syndrome
- Coagulation factor inhibitors
- Devic disease (neuromyelitis optica)
- Diabetic amyotrophy (diabetic proximal neuropathy or diabetic lumbosacral radiculoplexus neuropathy)
- Epidermolysis bullosa acquisita
- Epilepsy
- Graves ophthalmopathy
- Haemolytic disease of the newborn (HDN)
- Haemolytic transfusion reaction
- Hashimoto encephalopathy
- Limbic encephalitis — nonparaneoplasti
- Myocarditis in children
- Paediatric autoimmune neuropsychiatric disorder associated with streptococcal infection (PANDAS)
- Paraneoplastic neurological syndromes
- Potassium channel antibody-associated encephalopathy
- Pure red cell aplasia (PRCA)
- Pure white cell aplasia (PWCA)
- Pyoderma gangrenosum
- Rasmussen syndrome
- Scleromyxedema
- Sjogren’s syndrome
- Solid organ transplantation (other than kidney)
- Susac syndrome
- Systemic capillary leak syndrome (SCLS)
NO ROLE
Acute optic neuritis
Acute rheumatic fever
Adrenoleukodystrophy
Amegakaryocytic thrombocytopenia
Antiphospholipid syndrome (non-obstetric)
Aplastic anaemia/pancytopenia
Asthma
Atopic dermatitis/eczema — adult
Autism
Autologous haemopoietic stem cell transplantation
Behçet’s disease
Cardiac surgery with bypass — prophylaxis
Congestive cardiac failure
Crohn’s disease
Diamond Blackfan syndrome
Female infertility
Glomerulonephritis — IgA nephritis
Haemolytic uraemic syndrome
Henoch–Schonlein purpura
HIV/AIDS — adult
Idiopathic dilated cardiomyopathy
Linear IgA disease
Lupus cerebritis
Lupus nephritis
Motor neuron disease/amyotrophic lateral sclerosis
Myalgic encephalomyelitis
Narcolepsy/cataplexy
Nephrotic syndrome
Obsessive compulsive disorders
Polyneuropathy of critical illness
Recurrent foetal loss (with or without antiphospholipid syndrome)
Rheumatoid arthritis
Sepsis
Sickle cell disease
Systemic lupus erythematosus (SLE)
Ulcerative colitis